Online Journal
IF値: 0.898(2019年)→1.314(2020年)


Journal of Medical Ultrasonics

にて英文誌のFull textを閲覧することができます.


2007 - Vol.34

Vol.34 No.06

Case Report(症例報告)

(0587 - 0591)


A case of asymptomatic isolated noncompaction of the left ventricular myocardium

佐藤 早見1, 渡邉 百合1, 吉武 靖展1, 福島 敬子1, 植田 和子1, 尾田 敏恵1, 柏木 稔2, 眞柴 順子3, 大谷 規彰3, 林 靖生3

Hayami SATOU1, Yuri WATANABE1, Yasunobu YOSHITAKE1, Keiko FUKUSHIMA1, Kazuko UEDA1, Toshie ODA1, Minoru KASHIWAGI2, Jyunko MASHIBA3, Kisho OHTANI3, Yasuo HAYASHI3

1原三信病院生理検査室, 2原三信病院腎臓内科, 3原三信病院循環器科

1Cardiac Ultrasound Laboratory, Harasanshin General Hospital, 2Department of Nephrology, Harasanshin General Hospital, 3Department of Cardiology, Harasanshin General Hospital

キーワード : echocardiography, intertrabecular recesses, isolated noncompaction of the ventricular myocardium, magnetic resonance imaging


Noncompaction of the left ventricular myocardium is a rare congenital disorder characterized by the presence of numerous prominent trabeculations and intertrabecular recesses in the left ventricle. Clinical manifestations vary from no symptoms to congestive heart failure, arrhythmias, and thromboemboli. We report a case in which asymptomatic noncompaction of the left ventricular myocardium was considered likely. The patient was a previously healthy 31-year-old woman who presented with gross hematuria and was admitted to our hospital for renal biopsy. Perioperative echocardiograms demonstrated thinning and hypokinesis in the left ventricular inferior wall. Spongiform trabeculations were found in the inferior and posterior wall, and color flow Doppler studies confirmed the presence of blood flow within them. Cine magnetic resonance imaging showed prominent trabeculations and deep intertrabecular recesses. These findings were consistent with isolated noncompaction of the left ventricular myocardium. The patient has been asymptomatic and presented no major complications during 4 years of follow-up. Isolated noncompaction of the left ventricular myocardium is a cardiomyopathy that is more prevalent than previously reported. Combined echocardiographic and magnetic resonance imaging findings are important in the diagnosis of this entity. Because of the relatively high incidence of congestive heart failure, arrhythmias, and thromboemboli, their early diagnosis is important.