First Department of Internal Medicine, Akita University School of Medicine
Congestion, Doppler, Intestine, Protein C deficiency syndrome, Superior mesenteric artery
A 25-year-old man with distal myopathy was admitted to our institution because of sudden
abdominal pain. Color Doppler sonography showed a marked decrease in blood flow in the superior
mesenteric artery, leading to a diagnosis of intestinal congestion. This finding was confirmed by
subsequent angiographic examination. Laboratory tests indicated protein C deficiency (PCD).
Intensive medical treatment with warfarin improved the clinical symptoms and color Doppler findings
simultaneously. These results suggest that PCD should be considered in all cases of thromboembolic
disease of unknown origin, and that color Doppler sonography should be performed first when
patients with PCD have abdominal symptoms.