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英文誌(2004-)

Journal of Medical Ultrasonics

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1995 - Vol.22

Vol.22 No.02

Original Article(原著)

(0147 - 0151)

Focal Fatty Infiltrations in Chronic Hepatic Porphyria Without Skin Lesions

Hayato MlYACHI1, Mitsuhiro KUBOTA2, Hisae FUSEGAWA1, Shohei MATSUZAKI3, Yasuhiko ANDO1

1Department of Clinical Pathology Tokai University School of Medicine, 2Department of Surgery Tokai University School of Medicine, 3Department of Medicine Tokai University School of Medicine

キーワード : Alcoholic liver disease, Fatty liver, Porphyria, Ultrasonography

We studied ultrasonographic findings in nine patients with chronic hepatic porphyria. Seven of these patients had skin lesions characteristic of porphyria cutanea tarda, and the livers of all nine patients produced diffuse changes in parenchymal echoes that suggested the presence of chronic hepatitis, fibrosis, fatty change or cirrhosis, or other chronic liver disease associated with alcohol abuse, viral hepatitis, or both. Multiple nodular fatty infiltrations were detected in the livers of the two patients who had no skin lesions, and were confirmed on computed tomographic scan. Histologic findings were characteristic of chronic hepatic porphyria. Discovery of nodular fatty infiltrations through ultrasonographic examination is thus important in the diagnosis of chronic hepatic porphyria in patients without skin lesions.