岩田 守弘¹, 小林 秀樹², 村上 雅義², 千葉 喜英²

Morihiro IWATA¹, Hideki KOBAYASHI², Masayoshi MURAKAMI², Yoshihide CHIBA²

¹大阪大学医学部産婦人科学教室, ²国立循環器病センター周産期治療科

¹Department of Obstetrics and Gynecology, School of Medicine, Osaka University, ²National Cardiovascular Center

キーワード : Pulmonary atresia with intact ventricular septum, Prenatal diagnosis, Color flow mapping

Three cases of pulmonary atresia with intact ventricular septum were examined in vivo using color flow mapping for the purpose of antenatal diagnosis. In these cases, we observed the following findings: 1) extremely dilated right atrium, 2) marked tricuspid regurgitation, 3) blood flow signal in the pulmonary artery from the aorta through the ductus artery. So the blood flow direction was opposite to that normally present in the fetus.
Pulmonary atresia with intact ventricular septum consists of complete atresia of the pulmonary valve associated with intact ventricular septum. In pulmonary atresia with intact ventricular septum, pulmonary blood flow depends on the ductus arterious. Infants with this condition need immediate and special attention including administration of prostaglandins.