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英文誌(2004-)

Journal of Medical Ultrasonics

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2002 - Vol.29

Vol.29 No.04

Case Report(症例報告)

(J389 - J397)

超音波カラードプラ法が血行動態評価に有用であったBudd-Chiari症候群を合併した血管ベーチェット病の1例

Color Doppler Ultrasonography for Evaluating Hemodynamics in Budd-Chiari Syndrome Induced by Vasculo-Behcet's Disease

岩津 好隆1, 冨山 剛1, 関根 豊1, 吉澤 充代1, 菅野 健太郎1, 上沢 修2, 安田 是和3

Yoshitaka IWAZU1, Takeshi TOMIYAMA1, Yutaka SEKINE1, Mituyo YOSHIZAWA1, Kentaro SUGANO1, Osamu KAMISAWA2, Yoshikazu YASUDA3

1自治医科大学消化器内科, 2自治医科大学血管外科, 3自治医科大学消化器一般外科

1Department of Gastroenterology, Jichi Medical School, 2Department of Cardiovascular surgery, Jichi Medical School, 3Department of General surgery, Jichi Medical School

キーワード : Budd-Chiari syndrome, color Doppler ultrasonography, direct removal of thrombus, inferior vena cava thrombosis, vasculo-Behcet’s disease

A 31-year-old man had experienced repeated oral ulcerations since 1991, and genital ulceration and pain and swelling of the legs had started in September 2000. He was admitted to our institution in December 2000 complaining of back pain and abdominal distension. He had several aphthous lesions in the oral cavity, eruptions on the right leg, scarring from genital ulceration, and a positive needle reaction. Laboratory tests for inflammation and liver function were normal. Ultrasonography showed total occlusion of the hepatic portion of the inferior vena cava and the roots of the right hepatic vein, and thrombi in both sites. Color Doppler imaging showed blood flowing from the right hepatic vein to the middle hepatic vein, and regurgitation from the left hepatic veins. Portal flow drained into the veins of the abdominal wall through collaterals, predominantly through the paraumbilical vein. Thus our diagnosis was Budd-Chiari syndrome resulting from vasculo-Behcet's disease with thrombosis of the inferior vena cava. When liver function worsened despite initiation of medical treatment, including administration of prednisolone and anti-coagulation therapy, the occluded inferior vena cava and right hepatic vein were reconstructed by direct removal of the thrombus. Collateral flow decreased with normalization of flow in the inferior vena cava. However, thrombosis of the inferior vena cava recurred in the early postoperative period. Massive thrombosis from the inferior vena cava extended to all the hepatic veins, and collateral blood flow returned. Color Doppler imaging proved useful in evaluating the hemodynamics of this condition, but further evaluations will be necessary to determine the usefulness of direct removal of thrombi in vasculo-Bechet's disease.