We report a case of ectopia cordis with anencephalus that was diagnosed by ultrasonography at 13 weeks of gestation. This case had been caused by an amniotic band, which appeared as a linear echo between the fetal cardiac apex and the edge of the placenta. The various blood flows appeared in the cavities of the fetal heart, in front of the fetal thorax, on color flow mapping. The reversed flow of the vena cava was faster than that of a normal fetus, and the higher preload of the displaced heart was suspected of having been caused by the pressure of the amniotic fluid. Malformations of the skull, face, and thoracic and abdominal walls were found when the pregnancy was terminated at the 16 weeks of gestation. The amniotic band was attached to all lesions, and it had pulled the heart out of the trunk.